Alpha 1 - Antitrypsin Deficiency —— Biology-Pathogenesis-Clinical Manifestations-Therapy

----- Alpha 1-抗胰蛋白酶缺乏生物学-发病机制-临床表现-治疗

ISBN: 9780824788483 出版年：2014 页码：478 CRC Press

Providing a broad overview of basic and clinical aspects of alpha 1-antitrypsin (a 1AT) deficiency, this up-to-date reference discusses the complex pathobiological processes underlying the pathogenesis of a1AT deficiency, describes the a1AT gene and its promoter, and details specific therapies to prevent the major clinical manifestations of the dis